Component (or subunit) | Gene symbol | Chromosomal location | |
C1q: a chain | C1QA | 1p34.1-p36.3 | |
C1q: b chain | C1QB | 1p34.1-p36.3 | |
C1q: g chain | C1QG | 1p34.1-p36.3 | |
C8: a chain | C8A | 1p32 | |
C8: b chain | C8B | 1p32 | |
C4 Binding Protein: a chain | C4BPA | 1q32 (a) | |
C4 Binding Protein: b chain | C4BPB | 1q32 (a) | |
Complement Receptor 1 (CD 35) | CR1 | 1q32 (a) | |
Complement Receptor 2 (CD 21) | CR2 | 1q32 (a) | |
Decay Accelerating Factor (CD 55) | DAF | 1q32 (a) | |
Membrane Cofactor Protein (CD 46) | MCP | 1q32 (a) | |
Factor H | HF | 1q32 (a) | |
Factor I | IF | 4q25 | |
C6 | C6 | 5p13 (b) | |
C7 | C7 | 5p13 (b) | |
C9 | C9 | 5p13 (b) | |
C2 | C2 | 6p21.3 (c) | |
Factor B | BF | 6p21.3 (c) | |
C4A (isotype) | C4A | 6p21.3 (c) | |
C4B (isotype) | C4B | 6p21.3 (c) | |
C8: g chain | C8G | 9q22.3-q32 | |
C5 | C5 | 9q33 | |
Mannose Binding Lectin | MBL | 10q11.2-q21 | |
Perforin | PRF1 | 10q22 | |
Surfactant Proteins A1 and A2 | SFTPA1, A2 | 10q22-q23 | |
Surfactant Protein D | SFTPD | 10q22-q23 | |
Membrane
Inhibitor of Reactive Lysis
(MIRL, CD59) |
CD59 | 11p13 | |
C1 Inhibitor | C1NH | 11q11-q13.1 | |
C1r | C1R | 12p13 | |
C1s | C1S | 12p13 | |
Complement
Receptor 3: a chain,
= a-M Integrin (CR3A, CD11A) |
ITGAM | 16p11.2 | |
Vitronectin (S-protein) | VTN | 17q11 | |
C3 | C3 | 19p13.3-p13.2 | |
C5a receptor 1 | C5R1 | 19q13.3-q13.4 | |
Leucocyte
Adhesion Molecule: b chain,
= b-2 Integrin (LCAMB, CD18) |
ITGB2 | 21q22.3 | |
Properdin | PFC | Xp11.4-p11.2 |
Footnotes: | (a)
Regulators of complement activation (RCA) gene cluster
(b) Membrane attack complex (MAC) gene cluster (c) MHC class III complement gene cluster |